A case of bilateral congenital middle ear cholesteatoma.

Bilateral middle ear congenital cholesteatoma (CC) is an extremely rare disease. Middle ear CC grows from birth behind the intact ear drum, with no symptoms. Usually, it is detected by the pediatrician at the time of a routine visit. Undetected, it may grow for years until becoming quite large. Etiology of middle ear CC is still controversial, but it seems that an embryologic origin is the most acceptable. Progressive hearing loss and soft tissue density mass within the middle ear cavity usually differentiate the CC from other pathologies that include hearing loss and intact tympanic membrane. Treatment of CC requires early surgery and